* Evaluates the natural history of congenital heart lesions as a
background to finding out if and how much treatment has improved
outcomes
* Introduces and defines lesions, providing general information
about its frequency, familial or syndromic associations, and
associated congenital heart lesions
* Provides sections on pathological anatomy and physiology
– important in determining outcomes
* Includes results of surgery, both in terms of survival and also
in terms of event-free survival, that is, survival free of
reoperation, cardiac failure, arrhythmias, and other late
complications that are often seen
* Helps cardiologists and cardiac surgeons understand what is
likely to happen to patients with or without treatment, and which
forms of treatment currently in use provide the best outcomes to
date
Jadual kandungan
Foreword vii
Preface ix
Part 1 Introduction
1 Practical and Theoretical Considerations 3
2 Associated Noncardiac Problems 18
Part 2 Surgical Procedures
3 Aortopulmonary Shunts 25
4 Banding the Pulmonary Artery 33
5 Valves and Conduits 37
6 ‘Single Ventricle’ Repairs 57
7 Transplantation 71
Part 3 Left-to-Right Shunts
Section A Aortic Origin
8 Patent Ductus Arteriosus 79
9 Anomalous Origin of One Pulmonary Artery from the Aorta (Hemitruncus) 93
10 Aortopulmonary Window 97
11 Systemic Arteriovenous Fistula 103
12 Coronary Arterial Fistula 111
13 Congenital Aneurysms of the Sinus of Valsalva 121
Section B Ventricular or Atrial Origin
14 Atrial Septal Defect (Secundum) 133
15 Partial Anomalous Pulmonary Venous Connection with an Intact Atrial Septum 157
16 Scimitar Syndrome 161
17 Ostium Primum Defect 167
18 Complete Atrioventricular Septal Defect 175
19 Isolated Ventricular Septal Defect 183
20 Congenitally Corrected Transposition of the Great Arteries 206
Part 4 Obstructive Lesions
Section C Right Ventricular Outflow Tract
21 Pulmonary Stenosis 223
22 Double-Chambered Right Ventricle 234
23 Stenosis of the Main and Branch Pulmonary Arteries 237
Section D Left Ventricular Outflow Tract and Aorta
24 Valvar Aortic Stenosis 245
25 Bicuspid Aortic Valve without Stenosis 264
26 Supravalvar Aortic Stenosis 277
27 Discrete Subvalvar Aortic Stenosis 282
28 Coarctation of the Aorta 291
29 Interrupted Aortic Arch 318
Section E Left Ventricular Inflow Tract
30 Cor Triatriatum Sinister 329
31 Congenital Atresia or Stenosis of Pulmonary Veins 335
32 Congenital Mitral Valve Obstruction 341
Section F Regurgitant Lesions
33 Aortic Valve Regurgitation 353
34 Aortoventricular Tunnel 356
35 Mitral Valve Regurgitation 359
36 Tricuspid Valve Regurgitation 364
37 Idiopathic Pulmonary Regurgitation 368
Part 5 Miscellaneous Aortic Root Lesions
38 Anomalous Origin of a Coronary Artery from the Pulmonary Artery 373
39 Abnormal Origins of the Coronary Arteries from the Aortic Root 384
40 Vascular Rings and Slings 401
Part 6 Right-to-Left Shunts
41 Tetralogy of Fallot 413
42 Tetralogy of Fallot with Pulmonary Atresia 437
43 Tetralogy of Fallot with Absent Pulmonary Valve 446
44 Complete Transposition of the Great Arteries 451
45 Tricuspid Atresia 486
46 Pulmonary Atresia with Intact Ventricular Septum 494
47 Ebstein Anomaly 507
48 Truncus Arteriosus 519
49 Hypoplastic Left Heart Syndrome 531
50 Single (Double-Inlet) Ventricle 546
51 Double-Outlet Right or Left Ventricle 556
52 Total Anomalous Pulmonary Venous Connection 566
53 Heterotaxy Syndromes 579
54 Pulmonary Arteriovenous Fistula 587
55 Eisenmenger Syndrome 595
Index 605
Mengenai Pengarang
Julien I.E. Hoffman, M.D., B.SC. HONS., F.R.C.P
Professor of Pediatrics (Emeritus)
Senior Member, Cardiovascular Research Institute
Department of Pediatrics
University of California at San Francisco
San Francisco, CA
USA